OCT of OD showing degeneration of the photoreceptor outer segments irregularity and absence of the photoreceptor inner segment-outer segment (IS-OS) junction, loss of the outer nuclear layer, irregularity of the RPE, and decreased retinal thickness (arrows). The underlying pathogenic process is a degeneration of the photoreceptor outer segments.
The change seen in the retina corresponded to the scotoma. The loss of the IS-OS junction, loss of the outer nuclear layer, and thinning of the inner nuclear layer correlates with the area of visual field loss.
28 years of age, female; since 6 weeks photopsia with unaffected central vision; visual field defect at left eye in the superior temporal quadrant; intermitted headache. VA OD cc 0,9 , OS cc 0,9; IOP RA 14 mmHg, LA 14 mmHg
Ackermann, Andreas, Dr.med., Augenklinik, Universität Erlangen-Nürnberg, Erlangen, Deutschland; Mardin, Christian, Prof. Dr. med., Augenklinik, Universitätsklinikum Erlangen, Erlangen, Deutschland; Michelson, Georg, Prof. Dr. med., Interdisziplinäres Zentrum für augenheilkundliche Präventivmedizin und Imaging, Augenklinik, Friedrich-Alexander-Universität Erlangen-Nürnberg, Erlangen, Deutschland
