The white necrosis with fuzzy border occurs early in the disease and affects also the outer retinal layers. Soon pigment derangements and scarring of the retina develop. Several atrophic areas are already visible. Axons of the ganglion cells in the necrotic areas are visible as bright lines (arrows) along the normal course of the nerve fiber layer (Bjerrum Aerea). This disease occurs preferably in children who suffered from measles. Visial disturbances and peculiar behavior are early symptoms which lead to dementia and death.
