Atlas of Ophthalmology

North Carolina Macular Dystrophy

North Carolina Macular Dystrophy
Five year old girl with pigmented scar in fovea and surrounding atrophy of the pigment epithelium in the right eye (VA 0.1) and drusen in the left eye (VA 1.0). This is an autosomal dominant disease with complete penetrance. Lesions occur early in life and are mostly stationary. They reach from drusen-like features, disciform scars, sometimes with choroidal neovascularization to macular staphyloma.
Michael Cooney, M.D. and John Denny, M.D., Duke University Eye Center, Durham, NC, USA
H35.5
Retina -> Hereditary Degenerations and Dystrophies -> Retinal Pigment Epithelium (RPE) -> North Carolina Macular Dystrophy -> Case, North Carolina Macular Dystrophy
4683
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