Atlas of Ophthalmology

Congenital Macrovessels, Wyburn-Mason Syndrome

Congenital Macrovessels, Wyburn-Mason Syndrome
Convoluted and anastomosed enlarged vessels. It is very difficult to separate arteries from veins. Visual acuity is usually decreased. Hemorrhages and exudates may develop. When together with orbital or cerebral involvement it is called Wyburn-Mason syndrome
Cox, Terry, M.D., Duke Eye Ctr.¦2, Durham, NC, USA
Q86
Systemic Diseases -> Phakomatoses -> Wyburn-Mason Syndrome
congenital syndromes
6104
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