| Incontinentia Pigmenti (Bloch-Sulzberger) | |
| Initially, while a baby, dilated vessels and an avascular periphery lead to some peripheral proliferation and contraction which results in a dragged retina, a picture similar to retinopathy of prematurity (ROP). There can be multiple ocular abnormalities and CNS symptoms. Typical are areas of skin depigmention after initial vesicular eruptions. | |
| Lommatzsch, Peter, Prof. Dr. med., Univ.-Augenklinik, Leipzig, Germany | |
| H18.08, Q82.3 | |
| Congenital Syndromes, Malformations and Abnomalities -> Hereditary Syndromes -> Bloch-Sulzberger Syndrome (Incontinentia Pigmenti) | |
| congenital syndromes | |
| 6002 |
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